Request PDF on ResearchGate | On Jul 7, , Helvecio Leal Santos Júnior and others published AMILOIDOSE SISTÊMICA HEREDITÁRIA EM UM CÃO DA . Title: AMILOIDOSE SISTÊMICA EM AVES AQUÁTICAS CRIADAS EM CATIVEIRO. (Portuguese); Alternate Title: Systemic amyloidosis in captive waterfowls. Os autores apresentam um caso de amiloidose sistémica com envolvimento cardíaco e discutem a importância de um elevado índice de suspeição para o.

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The composition of such amyloid substances, in addition to fibrils, although formed by different types of proteins and carbohydrates presents some common aspects: Since then she started presenting new lesions in outbreaks, always in the same places.

Pulmonary amyloidosis: computed tomography findings

Methods San Diego, Calif. The patient was referred to a hematology service for multiple myeloma treatment. Calcitonina [ 15 ]. New fibres from proteins.


Correlation with cardiac amyloidosis. How to cite this article.


Sistdmica New England Journal of Medicine 6: J Eur Acad Dermatol Venereol. Merkel, and Lynne Regan Consultado o 25 de decembro de We report a case of systemic amyloidosis associated with multiple myeloma, which was diagnosed based on the cutaneous symptom complex. Primary pulmonary amyloidosis as a cause of interlobular septal thickening.

Published online February History of the Amyloid Fibril”. Such lesions worsened when there was local trauma.

Primary systemic amyloidosis associated with multiple myeloma

Full-length rat amylin forms fibrils following substitution of single residues from human amylin. Among the abnormal tests, we found: Approved by the Advisory Board and accepted for publication on They affect mainly the eyelids, lips, tongue, oral siste,ica, neck, axillae, umbilical scar and retroauricular, inguinal and anogenital regions.

In contrast, in the secondary systemic form the amyloid deposition takes place above all in parenchymatous organs: Cranium and long bones X-rays did not reveal lytic lesions.

Beta-amiloide [ 7 ] [ 8 ] [ 9 ]. Espazos de nomes Artigo Conversa.

Am J Med ; Type and distribution of pulmonary parenchymal and vascular amyloid. The first lesions appeared following emotional stress and regressed spontaneously within 15 days.


Congo red staining confirmed it was an amyloid substance Figures 4 and 5. Thus it was possible to make the diagnosis of multiple myeloma in the initial phase in a patient that presented only cutaneous manifestations of amyloidosis.

During the physical examination confluent papules of varied sizes were observed in the internal half of upper eyelids and more discreet in the internal corner of the lower eyelids Figure 1. Current molecular medicine 8 6: All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. In primary systemic amyloidosis, the deposit occurs predominantly in tissues such as in the gastrointestinal tract, smooth and skeletal muscles, carpal connection, nerves and skin.

High-resolution CT of the lung.